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Cystic Fibrosis
Fibrocystic Disease of Pancreas | Mucoviscidosis | Pancreatic Cystic Fibrosis | Cystic Fibrosis, Pancreatic | Fibrosis, Cystic | Fibrosis, Pancreatic Cystic | Mucoviscidoses | Pancreas Fibrocystic Disease | Pancreas Fibrocystic Diseases
An inherited disease of exocrine glands, affecting most characteristically the pancreas, respiratory system, and sweat glands, usually beginning in infancy and typified by chronic respiratory infections, pancreatic insufficiency, and susceptibility to heat prostration. Cirrhosis of liver occurring in childhood is common and may produce portal hypertension, splenomegaly, and hypersplenism. |
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